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ColunaTipoPK
idTEXT
descricaoTEXT
codigoTEXT
tipo_agravo_idTEXT
sexo_esus_idTEXT
esus_idINTEGER
ativoINTEGER
data_criacaoTEXT
data_alteracaoTEXT
iddescricaocodigotipo_agravo_idsexo_esus_idesus_idativodata_criacaodata_alteracao
27b8c631-941d-4ad1-8aae-fea180b7d218Síndrome da deficiência congênita de iodo do tipo mistoE002708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c168312021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
25ac3484-cb76-4983-822d-5efa660f5257Transtorno hemorrágico devido a anticoagulantes circulantesD683708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c159412021-05-25T19:40:03.594000+00:002021-05-25T19:40:03.594000+00:00
caa59285-a146-435e-b4f5-3cc296713399Outros defeitos especificados da coagulaçãoD688708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c159612021-05-25T19:40:03.594000+00:002021-05-25T19:40:03.594000+00:00
2cac4f47-6c42-4968-835d-a008174eddabDefeito de coagulação não especificadoD689708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c159712021-05-25T19:40:03.594000+00:002025-11-03T17:53:51.492000+00:00
09698b8e-0abb-483b-8d95-008edeb82ed5Linfohistiocitose hemofagocíticaD761708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c163012021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
2a627294-8b57-4918-8fee-76f89e8d7e9fImunodeficiência combinada grave [SCID] com números baixos de células T e BD811708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164512021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
e0e997a5-8823-4584-9c26-555fe072c292Imunodeficiência combinada grave [SCID] com números baixos ou normais de células BD812708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164612021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
d5b4b74d-13a4-4bff-b117-a0267019b441Hipogamaglobulinemia transitória da infânciaD807708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164112021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
8aee58de-eb67-41b0-865f-75e5628ac1b6Outras imunodeficiências com predominância de defeitos de anticorposD808708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164212021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
576fab82-4be0-4844-b9ff-d87ea34db50cImunodeficiência não especificada com predominância de defeitos de anticorposD809708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164312021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
29145915-9d20-4958-9151-9a81f6643dc4Deficiência de adenosina-deaminase [ADA]D813708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164712021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
1f523c3d-e7dc-424a-8e77-7a0d1d358b8eSíndrome de nezelofD814708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164812021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
bce299e1-33dd-4d54-a12c-45d4ffc0c422Deficiência de purina-nucleosídeo fosforilase [pnp]D815708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164912021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
039dbb9e-5187-4a6d-874f-715172abac7bDeficiência major classe I do complexo de histocompatibilidadeD816708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165012021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
fc5a0677-e13d-47d7-9730-b17567e830faDeficiência major classe II do complexo de histocompatibilidadeD817708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165112021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
a6f896e6-1c3d-400c-9a55-8773957654e0Outras deficiências imunitárias combinadasD818708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165212021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
47a1f3d4-b7fe-4914-86a2-19de3a99708fDeficiências imunitárias combinadas não especificadasD819708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165312021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
448afc88-0f3e-4acb-af79-ec7a01baa7f1Imunodeficiência associada com outros defeitos majorD82708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1271912021-05-25T19:40:03.700000+00:002021-05-25T19:40:03.700000+00:00
1327cf36-886f-4f90-878f-d5d43bc51fd8Síndrome de Wiskott-AldrichD820708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165412021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
334c6b40-a303-4642-82e6-24cb270d0570Síndrome de di GeorgeD821708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165512021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
c16e80a6-149a-4aea-b20b-c8d8229cd664Imunodeficiência com encurtamento de membrosD822708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165612021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
9bbfd4d8-5e04-4271-b74c-db2e276121f6Síndrome da hiperimunoglobulina E [IGE]D824708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165812021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
6490053f-31ff-40d7-b18b-93a908fa9ea9Imunodeficiências associadas com outros defeitos major especificadosD828708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c165912021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
1a99284a-d092-4c39-a742-22f4f7b2612cImunodeficiência associada com defeitos major não especificadosD829708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166012021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
218263b0-a987-49b8-a2d1-55e0af2a8eeeImunodeficiência comum váriavelD83708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1272012021-05-25T19:40:03.690000+00:002021-05-25T19:40:03.690000+00:00
9465fcca-5f38-4ff0-ba16-672a82c4b597Imunodeficiência comum variável com predominância de anormal. do número e da função das células BD830708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166112021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
cc26bdfd-445a-4018-a9be-b76e569a8290Imunodeficiência comum variável com predominância de transtornos imunorregulatórios de células TD831708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166212021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
f37e4bc1-116d-4d70-83f7-a86eb4025b1aImunodeficiência comum variável com auto-anticorpos às células B ou TD832708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166312021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
f8d683f4-180e-4673-b880-ebabf3f0151eOutras imunodeficiências comuns variáveisD838708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166412021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
b9eea2e0-08da-4fa8-a0ed-dd72aaf83663Imunodeficiência comum variável não especificadaD839708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166512021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
b4770124-3481-4582-bd5e-7ca236cd6074Outras imunodeficiênciasD84708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1272112021-05-25T19:40:03.690000+00:002021-05-25T19:40:03.690000+00:00
7f296469-134e-4ec9-9099-a3a926bb63d2Defeito do antígeno-1 da função de linfócito [LFA-1]D840708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166612021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
c8ac2af5-cc34-46e0-bbba-c4beecae5f5aDefeitos no sistema complementoD841708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166712021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
da2ad438-92d5-40e0-aa98-5298c2b13d8cOutras imunodeficiências especificadasD848708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166812021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
7b22fb6c-b5a1-485a-bc87-bb498272bb32Imunodeficiência não especificadaD849708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c166912021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
14a611d9-4cb3-4225-9336-126d129c178bSarcoidoseD86708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1272212021-05-25T19:40:03.690000+00:002021-05-25T19:40:03.690000+00:00
dcd9cf15-9c2a-40ae-8a67-633a7b7dd7e6Sarcoidose do pulmãoD860708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167012021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
d7ae12f5-4d6e-4c8e-96c8-5839a15e30ceSarcoidose dos gânglios linfáticosD861708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167112021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
662f6faf-8f57-4816-9c68-459731e694d1Sarcoidose do pulmão com sarcoidose dos gânglios linfáticosD862708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167212021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
7338ccb1-b284-4458-a73c-44aca1535a50Sarcoidose da peleD863708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167312021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
dafc2df3-1ff2-4864-90b7-6b54aab230cbSarcoidose de outros locais especificados e locais combinadosD868708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167412021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
5f026b21-b4aa-4d26-9a3e-8526df0603fcSarcoidose não especificadaD869708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167512021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
475f43f0-48b9-4c1a-9629-c8d70188f5d1Outros transtornos que comprometem o mecanismo imunitário não classificados em outra parteD89708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1272312021-05-25T19:40:03.690000+00:002021-05-25T19:40:03.690000+00:00
b50abe93-1bdc-4ea3-9fc7-e39c7e2a8e93Hipergamaglobulinemia policlonalD890708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167612021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
a23d3c38-5591-4c71-950e-acdc6e1e2e57Hipergamaglobulinemia não especificadaD892708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167812021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
67163302-d12f-4b58-86a6-8e8bb0a70124Outros transtornos especificados que comprometem o mecanismo imunitário ñ classificados noutra parteD898708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c167912021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
36b8ab2b-b944-400d-a798-f45f44e7d356Síndrome de deficiência congênita de iodoE00708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1272412021-05-25T19:40:03.690000+00:002021-05-25T19:40:03.690000+00:00
7fb430ff-cbdf-4b17-a9b6-a5959b41f50fDeficiências imunitárias combinadasD81708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c1271812021-05-25T19:40:03.690000+00:002021-05-25T19:40:03.690000+00:00
25ea06a8-9839-46fa-a9ac-d048447406b7Imunodeficiência combinada grave [SCID] com disgenesia reticularD810708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c164412021-05-25T19:40:03.595000+00:002021-05-25T19:40:03.595000+00:00
4146b563-f9cd-4752-a669-5cdbeaf3f0a4Tireotoxicose factíciaE054708dcbc4-baf1-4882-8fb6-24914a6c152ef8641bf6-74cd-4bb9-be22-22cbb555885c170712021-05-25T19:40:03.596000+00:002021-05-25T19:40:03.596000+00:00